This A 45-year-old divorced white male came to the emergency room with severe hepatic cirrhosis and aspiration pneumonia. Shortly after admission he developed cardiac arrhythmias and died. Significant past history included alcohol abuse, cirrhosis, and neurofibromatosis. He had no family history of neurofibromatosis, but his condition was diagnosed at age 17 when he developed neurofibromas along the lateral chest wall. There was no history of continued follow-up after this initial diagnosis.

== Autopsy Findings ==The patient was covered with variably sized subcutaneous nodules ranging from 0.5 to 2.5 cm in diameter. Other significant findings included micronodular hepatic cirrhosis (liver weight: 1760 grams), ascites (500 ml), and splenomegaly (weight: 260 grams).

File:IPLab5Neurofibromatosis1IPLab5Neurofibromatosis1b.jpgJPG|This photograph, taken at autopsy, demonstrates the distribution of neurofibromas on the skin of this patient. File:IPLab5Neurofibromatosis2IPLab5Neurofibromatosis2b.jpgJPG|This is another view taken at autopsy demonstrating the neurofibromas. Some lesions can be seen as subcutaneous swellings (arrow) and others form pedunculated masses. Most are hyperpigmented. File:IPLab5Neurofibromatosis3IPLab5Neurofibromatosis3b.jpgJPG|This is a closer view of neurofibromas on the skin.