PEIR Digital Library

Welcome to the Pathology Education Informational Resource (PEIR) Digital Library, a multidisciplinary public access image database for use in medical education.

Home / Tag cystic fibrosis /


00134064.jpg 00134065 Thumbnails 00133516 00134065 Thumbnails 00133516

RADIOLOGY: KIDNEY: Case# 33662: AUTOSOMAL RECESSIVE POLYCYSTIC KIDNEY DISEASE. 2 month old male with oliguria and history of prenatal oligohydramnios. The kidneys are enlarged bilaterally and there is diffuse brightly increased renal parenchymal echogenicity. There is no distinct corticomedullary junction. No hydronephrosis is identified. Recessive type polycystic kidney disease is also known as infantile polycystic kidney disease. This is usually a combination of renal and hepatic manifestations and presents in infancy. Pathologically, the kidney has innumerable small cysts that represent dilatation of the collecting tubules. Liver involvement results in proliferation of bile ducts and mild periportal fibrosis. The diagnosis should be suspected when the kidneys are enlarged and hyperechoic and the bladder is small, especially in the prenatal setting of oligohydramnios.

Peter Anderson
Rating score
no rate
Rate this photo